This is a rare, congenital or/and acquired skin disease with associated other manifestations, and loose redundant skin mainly showed disorders of elastic fiber in skin.
Recently we have experienced a ram of 25 years old female with skin laxity and fold involved to the face, neck, ear and dorsum of hand. And also mild geneneralzed involvement of other part of skin.
Characteristically, the exposed area was more old looking skin than the hidden part of the remaining skin but histologically the abnormal involvement of the skin and internal organs were proved the abnormal histological finding are as follows, elastic fibers are diminished markedly in face skin, its scar, and slightly in abdominal skin, but partially in appendix and some blood vessels.
Authors operated on this case twice for only cosmetic purpose such as total rhytidectomy of the face after surgery, the result was satisfactory but still the skin problems remains.
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